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患儿女,7岁。因皮肤发硬半年,关节屈曲、僵硬、疼痛、活动障碍2月入院。病前2周有发热、咳嗽、腹泻史。家族史无特殊。体检:体温38℃、血压14.7/9.3kpa、精神较差,面色腊黄,表情固定,面颊、颈后、躯干、四肢、耻骨联合等处皮肤紧张,肥厚如硬橡皮,不易捏起。其表面,部份有褐色色素沉着,小腿皮肤有片状脱屑。心肺无异常。腹部膨满、腹壁静脉怒张,肝脏在肋下锁骨中线6厘米,剑突下4.5厘米,边缘钝、光滑、质
Children with children, 7 years old. Due to skin stiff six months, joint flexion, stiffness, pain, mobility disorder in February admission. 2 weeks before illness, fever, cough, history of diarrhea. No special family history. Physical examination: Body temperature 38 ℃, blood pressure 14.7 / 9.3kpa, poor spirit, looking yellow, facial expressions, cheeks, neck, trunk, limbs, pubic symphysis and other skin tension, hypertrophy such as hard rubber, easy to pinch. The surface, some brown pigmentation, calf skin flake scaling. No abnormal heart and lung. Abdominal swelling, abdominal venous distention, the liver in the subclavian midline clavicle 6 cm, 4.5 cm under the xiphoid, blunt edge, smooth, quality