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病历摘要患者男,41岁,因头昏、乏力伴尿黄20余天于1980年5月29日首次入院。入院前数日食蚕豆,未服任何药物。既往无蚕豆过敏史,无疟疾史,无黄疸及出血史,曾赤脚参加田间劳动。父母双亡(死因不详)。查体:呈贫血貌,巩膜轻度黄染,肝肋下1cm,脾肋下1.5cm,质Ⅱ°。实验室检查:RBC 260万/mm~3,Hb 6克%,网织红细胞4.8%,血小板9.2万/mm~3,WBC6700/mm~3,N55%L37%,E 8%,红细胞脆性试验:开始溶血0.40%完全溶血<0.28%,肝功能:黄疸指数12u,尿胆
Patient, male, 41 years old, first hospitalized on May 29, 1980 due to dizziness, fatigue and urinary yellow 20 days. Eat broad beans several days before admission, did not take any medication. Past no broad bean allergy history, no history of malaria, no history of jaundice and bleeding, had barefoot to participate in field work. Parents died (unknown cause of death). Physical examination: anemia appearance, scleral mild yellow dye, liver ribs 1cm, spleen rib 1.5cm, quality Ⅱ °. Laboratory tests: RBC 2.6 million / mm ~ 3, 6% Hb, reticulocyte 4.8%, platelet 92,000 / mm ~ 3, WBC6700 / mm ~ 3, N55% L37%, E8%, erythrocyte fragility test: Hemolysis began 0.40% complete hemolysis <0.28%, liver function: jaundice index 12u, urine