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有关溶血尿毒综合征和血栓性血小板减少性紫瘢发病机理的最新理论是:血管内皮细胞产生前列腺环素(简称PGI_2)所必需的血浆因子的缺乏或血循环中存在着抑制PGI_2的物质,或者两者都起作用。成人溶血尿毒综合征患者发现缺乏PGI_2支持这些概念。血浆除去法即用正常血浆交换治疗的有效性可能由于替换一种缺乏的血浆因子或去除一种抑制因子。作者用血浆除去法治疗儿童溶血尿毒综合征后的发现与此争论有关。病例报告:男,3(1/2)岁,无咳嗽、厌食和呕吐病史。住院时有贫血和脱水,并伴有广泛的紫瘢。血红
The latest theory about the pathogenesis of hemolytic uremic syndrome and thrombotic thrombocytopenic purpura is the lack of plasma factors necessary for the production of prostacyclin (referred to as PGI 2) by vascular endothelial cells or the presence of substances that inhibit PGI 2 in the blood circulation, or two All work. Patients with adult hemolytic uremic syndrome have been found to lack PGI2 in support of these concepts. The effectiveness of plasma removal, ie, treatment with normal plasma exchange, may be due to the replacement of a deficient plasma factor or the removal of an inhibitory factor. The authors found that the use of plasma removal of hemolysis-induced uremic syndrome in children with this controversy. Case Report: Male, 3 (1/2) years old, without history of cough, anorexia and vomiting. Anemia and dehydration when hospitalized, accompanied by a wide range of purple scar. Blood red