经扁平部玻璃体切除术治疗视乳头旁的视网膜毛细血管瘤

• 作 者: Kreusel K.-M. Bechrakis N.E. Neumann H.P.H. Foerster M.H. 邢咏新
• 机 构: Gurnemanzpfad 93 Berlin 13465,Germany Dr.,
• 出 处: 世界核心医学期刊文摘.眼科学分册
• 发表日期: 2006年Z1期
• 关键词: 玻璃体切除术 毛细血管瘤 乳头 视网膜前膜 视功能 肿瘤切除术 医学检查 预后良好 族性 肿瘤复发

PURPOSE: To describe the treatment of juxtapapillary capillary angioma by pars plana vitrectomy (PPV) and tumor excision. DESIGN: Interventional case report. METHODS:A6-year-old girl with symptomatic juxtapapillary capillary retinal angioma with associated epiretinal membrane (ERM) underwent PPV and extraction of the tumor and ERM. A clinical and molecular genetic workup for the presence of von Hippel-Lindau disease (VHL) was performed. RESULTS: A favorable functional result without tumor recurrence was achieved. Capillary retinal angioma was confirmed by histology of the surgical specimen,and familial VHL was revealed. CONCLUSIONS: PPV and extraction of the tumor is applicable in juxtapapillary capillary retinal angioma with associated ERM. A workup for the presence of VHL is pertinent in patients presenting with this tumor entity.

METHODS: A6-year-old girl with symptomatic juxtapapillary capillary retinal angioma with associated epiretinal membrane (ERM) underwent PPV A clinical and molecular genetic workup for the presence of von Hippel-Lindau disease (VHL) was performed. RESULTS: A favorable functional result without tumor recurrence was achieved. Capillary retinal angioma was confirmed by histology of the surgical specimens, and familial VHL was revealed. CONCLUSIONS: PPV and extraction of the tumor is applicable in juxtapapillary capillary retinal angioma with associated ERM. A workup for the presence of VHL is pertinent in patients presenting with this tumor entity.