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近年来,骨髓移植治疗取得较大进展。它的临床应用除了再生障碍性贫血和急性白血病外,许多国外学者应用骨髓移植成功治疗某些先天性疾病,如严重联合免疫缺陷病、地中海贫血、幼年性骨硬化病和网状系统发育不全症等。骨髓移植的应用为这些疾病的治疗开辟了新的途径。本文就此作一简单的文献复习。网状系统发育不全症网状系统发育不全症是严重的联合免疫缺陷病。它通常以先天性粒细胞缺乏、淋巴细胞缺乏、淋巴样组织和胸腺发育不全及细胞和体液免疫功能缺陷为特征。患儿多于出生
In recent years, bone marrow transplantation has made great progress. Its clinical application In addition to aplastic anemia and acute leukemia, many foreign scholars apply bone marrow transplantation for the successful treatment of certain congenital diseases such as severe combined immunodeficiency disease, thalassemia, juvenile sclerosis and reticular phyllosis Wait. The use of bone marrow transplantation opens up new avenues for the treatment of these diseases. This article for a simple review of the literature. Reticulopathies Reticulopathies are severe combined immunodeficiency disorders. It is often characterized by a lack of congenital agranulocytosis, lymphocytic deficiency, hypoplastic lymphoid tissue and thymus, and defects in cellular and humoral immunity. More children than born