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噬血细胞综合征(hemophagocytic syndrome,HS)是一组从骨髓细胞学角度提出的病征,其临床和实验室特点颇似恶组,而两者的治疗和预后有明显差异。国外已引起重视,现将遇到的2例报告如下: 1 病例报告【例1】患者男,35岁,教师,已婚。困乏力,畏寒、发热伴颈部肿物7d入院。查体:T39.4℃,R 22次/min,P102次/min,BP16/10kPa,急性重病容,双颌下、颈部、锁骨上、腋、腹股沟可触及小指头大的淋巴结,咽充血,左侧咽部可见一脓点,双侧扁桃体I°肿大、充血。胸骨无压痛,心肺未见异常,腹软,肝肋下2cm,脾肋下2cm,腹水征阴性。化验:Hb 142g/L,WBC1.36×10～9/L,N0.54,L0.46,RL0.005,BPC103×10～9/L。B超示肝脾肿大,腹腔淋巴结
Hemophagocytic syndrome (HS) is a group of syndromes characterized by bone marrow cytology. Its clinical and laboratory features are quite similar to those of the malignant group, and the treatment and prognosis of the two are obviously different. Abroad has attracted attention, the two cases are now reported as follows: 1 case report [Example 1] Male patient, 35 years old, teacher, married. Sleepy, chills, fever with neck mass 7d admission. Examination: T39.4 ℃, R 22 times / min, P102 times / min, BP16 / 10kPa, acute serious illness, double submandibular, neck, supraclavicular, axilla, groin can reach the little finger big lymph nodes, pharyngeal congestion , Left pus can be seen a pus point, bilateral tonsil enlargement I, congestion. Sternal no tenderness, heart and lung no abnormalities, abdominal soft, liver ribs 2cm, spleen ribs 2cm, ascites sign negative. Assay: Hb 142g / L, WBC 1.36 × 10 ~ 9 / L, N0.54, L0.46, RL0.005, BPC103 × 10 ~ 9 / L. B ultrasound shows hepatosplenomegaly, abdominal lymph nodes