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目的:探讨原发性气管支气管淀粉样变的流行病学特征、临床表现及诊断和治疗方法。方法:回顾1例原发性气管支气管淀粉样变病例的临床特点,并结合文献进行分析。结果:患者主要表现为咳嗽、咳痰、咯血及呼吸困难,经纤支镜活检标本刚果红染色阳性。经治疗后患者症状明显缓解。结论:原发性气管支气管淀粉样变临床上发病率极低,容易误诊,组织病理学检查是气管支气管淀粉样诊断的金标准,目前缺乏特异性治疗方法。
Objective: To explore the epidemiological features, clinical manifestations, diagnosis and treatment of primary tracheobronchial amyloidosis. Methods: The clinical features of one case of primary tracheobronchial amyloidosis were retrospectively analyzed and analyzed. Results: The patients mainly showed cough, sputum, hemoptysis and dyspnea. Congo red staining was positive with fiberoptic biopsy specimens. After treatment, the patient’s symptoms were relieved. Conclusions: The incidence of primary tracheobronchial amyloidosis is extremely low and easily misdiagnosed. Histopathology is the gold standard for the diagnosis of tracheobronchial amyloidosis. Currently there is no specific treatment.