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患者谢×,女性,21岁,干部。以间歇性巩膜、皮肤黄染19年为主诉于1979年11月9日入院。患者2岁时经家人发现巩膜发黄而住入某院传染科,经检查确系黄疸但无症状,接受一般护肝治疗后出院。此后,黄疸间歇存在,尚能照常工作与劳动,但体力较差,易疲乏。每因疲劳、上呼吸道感染及胃肠炎症后,黄疸可加深,然无皮肤搔痒、大便颜色变浅等症。无消化不良、肝区疼痛及发热等症状。否认疟疾史。据其父云,其妹似有眼睛发黄,但身体健康。体格检查:发育正常,营养一般。无贫血外观。巩膜、皮肤轻度黄染。心、肺(一)。腹部柔软,无压痛点,肝、脾未触及。实验室检查:血红蛋白11克％,网状红细胞0.3％,红细胞脆性试验;0.40％氯化钠溶液开始溶血,0.34％完全溶血。热溶血试验、酸溶血试验、Coombs试验均阴性。骨髓象正常。肝功能试验:黄疸指数18单位,范登堡氏试验直接迅速阳性,胆红素总量3.0mg,结合胆红素2.0mg,絮状、浊度阴性。硷
Patient Xie ×, female, 21 years old, cadre. Intermittent sclera, skin yellow dye 19-year-old chief complaint on November 9, 1979 admission. At 2 years old, his family found that the sclera was yellow and admitted to a hospital infection department. The examination confirmed that the jaundice was asymptomatic and was generally discharged after receiving liver protection. Since then, jaundice intermittent presence, still able to work and work as usual, but physically poor, easy to fatigue. Because of fatigue, upper respiratory tract infection and gastrointestinal inflammation, jaundice may deepen, but no skin itching, stool color and other embolisms. No indigestion, liver pain and fever and other symptoms. Denied the history of malaria. According to his father cloud, his sister seems to have yellow eyes, but good health. Physical examination: normal development, general nutrition. No anemia appearance. Sclera, skin mild yellow dye. Heart, lung (a). Abdomen soft, no tenderness point, liver, spleen not touched. Laboratory tests: 11 grams of hemoglobin, reticulocyte 0.3%, red blood cell fragility test; 0.40% sodium chloride solution began to hemolysis, 0.34% complete hemolysis. Hemolysis test, acid hemolysis test, Coombs test were negative. Bone marrow as normal. Liver function test: 18 units of jaundice index, Vandenberg test directly and rapidly positive, total bilirubin 3.0mg, bilirubin 2.0mg, flocculent, turbidity negative. base