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角膜上皮基底膜营养不良是一常染色体显性遗传性眼病。近来作者遇到2例,均系误诊病例,后经病理证实为该病。例1 陈××男30岁农民住院号288576 近年来,双眼反复发作性疼痛,视力逐渐下降,每年发作数次,每次持续1周左右而自然缓解。右眼视力0.04,左眼0.01。裂隙灯检查可见双眼有弥漫性上皮剥脱及上皮性点状、地图状及斑块状图像,用宽光带检查,可发现图像边缘清晰,呈暗灰色。角膜实质及内皮均正常。荧光素染色上皮剥脱区染色外,其余病灶均不着色。家族成员无类似眼病。诊断“双眼环形角膜营养不良”。住院后行左眼穿透角膜移值术。病理诊断为角膜上皮基底膜营养不良。
Corneal epithelial basement membrane dystrophy is an autosomal dominant inherited eye disease. Recently, the author encountered two cases, all were misdiagnosed cases, confirmed by the pathology of the disease. Example 1 Chen × × male 30-year-old farmer hospitalization 288576 In recent years, eyes repeatedly recurrent pain, visual acuity decreased gradually attack several times a year, each lasting for about 1 week and naturally relieve. Right eye visual acuity 0.04, left eye 0.01. Slit lamp examination showed diffuse epithelial epithelial exfoliation and epithelial punctate, map-like and plaque-like images, with a wide band check, you can find the image edge clear, dark gray. Corneal parenchyma and endothelium are normal. Fluorescein staining epithelial stripping area staining, the remaining lesions are not colored. Family members have no similar eye disease. Diagnosis of “Coronal Corneal Malnutrition.” Left eye after corneal transposition surgery. Pathological diagnosis of corneal epithelial basement membrane malnutrition.