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Prion病是指由于细胞内正常型Prion蛋白发生高级结构变换,成为变异型Prion蛋白而引发疾病的总称。已知的人类Prion病包括人克雅病(Creutzfeld-Ja-kob disease,CJD)、Gerstmann-Straussler-Scheinker综合征(Gerstmann-Straussler-Scheinker syndrome,GSS)、致死性家族性失眠症(f
Prion disease is a general term for disease caused by the high-level structural transformation of normal intracellular Prion protein into a variant Prion protein. Known human Prion diseases include Creutzfeld-Ja-kob disease (CJD), Gerstmann-Straussler-Scheinker syndrome (GSS), fatal familial insomnia (f