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目的 对照病理诊断探讨小儿间质性肺疾患 (ILD)的临床表现及特点。方法 总结 1996～ 2 0 0 2年经开胸肺活检诊断的 3例小儿ILD的临床表现、影像学及病理学的特点并进行文献复习。结果 3例ILD患儿 ,男 2例 ,女 1例 ,年龄 7～ 11岁 ,就诊时病程 1～ 3个月 ,临床主要表现为咳喘、胸闷憋气、发热和杵状指等。 3例患儿X线胸片、胸部高分辨CT均有肺纤维化表现 ,病理诊断分别为脱屑性间质性肺炎 (DIP)、淋巴细胞间质性肺炎(LIP)、非特异性间质性肺炎 (NSIP)。结论 对不易明确诊断的有干咳、气促、呼吸困难等症状的患儿应强调做开胸肺活检
Objective To investigate the clinical manifestations and characteristics of children with interstitial lung disease (ILD) according to pathological diagnosis. Methods The clinical manifestations, imaging features and pathological features of 3 pediatric ILD diagnosed by thoracotomy for lung biopsy from 1996 to 2002 were reviewed and reviewed. Results 3 cases of ILD children, 2 males and 1 females, aged 7 to 11 years, the duration of treatment of 1 to 3 months, the main clinical manifestations of cough, chest tightness, suffocation, fever and clubbing and so on. Three cases of children with chest X-ray, high-resolution chest CT showed pulmonary fibrosis, pathological diagnosis of asymptomatic interstitial pneumonia (DIP), lymphocyte interstitial pneumonia (LIP), non-specific interstitial Pneumonia (NSIP). Conclusions Children with symptoms such as dry cough, shortness of breath, difficulty breathing and other symptoms that are not easily diagnosed should be emphasized on open lung biopsy