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多数毕夏氏综合征病例,眼均受累。一般眼部表现有反复发作性虹膜睫状体炎、视神经萎缩、视网膜血管管腔变狭窄且有白鞘、视网膜出血,病情恶化,甚至眼球萎缩,终而失明。在全身表现有口腔及阴部粘膜溃疡、结节性红斑、静脉栓塞、皮肤脓疡、关节病及皮肤非特异性过敏等,如中枢神经系统被侵犯,生命预后极其严重。70年作者报告11例,用苯丁酸氮芥(Chlo-rambucil,瘤可宁)治疗,病情控制。本文报告其中5例追随观察情况,并增加9例,共14例的治疗效果。
Most cases of Bi syndrome, eyes are involved. General ocular manifestations of recurrent iridocyclitis, optic atrophy, retinal vascular lumen narrowing and a white sheath, retinal hemorrhage, exacerbations, and even the eye atrophy, and eventually blindness. Oral and perineal mucosal ulcers, nodular erythema, venous thrombus, skin abscess, arthrosis and skin nonspecific allergies are all manifestations of the oral cavity and pudendal mucosa. If the central nervous system is violated, the prognosis of life is extremely serious. Seventy years of the authors reported 11 cases treated with Chlo-rambucil (TM) and condition control. This article reports 5 cases follow the observation, and an increase of 9 cases, a total of 14 cases of treatment.