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目的探讨胰腺血管周上皮样细胞肿瘤(PEComas)的临床病理特点、影像学改变及鉴别诊断。方法对1例胰腺PEComas进行影像学、病理形态学及免疫组化标记观察并复习相关文献。结果肿瘤主要由上皮样细胞构成,绕血管呈巢状或片状排列,富含厚壁及薄壁血管,未见明显坏死和核分裂象。结论胰腺PEComas是一种生物学行为未定的间叶源性肿瘤,以女性多见,有其独特的组织形态和免疫表型。目前以手术完整切除为主要治疗方法,术后应密切随访。
Objective To investigate the clinicopathological characteristics, imaging changes and differential diagnosis of pancreatic perivascular cell carcinomas (PEComas). Methods One case of pancreatic PEComas was observed by imaging, histopathology and immunohistochemistry. The related literatures were reviewed. Results The tumors mainly consisted of epithelioid cells, arranged in nests or flakes around blood vessels, and were rich in thick and thin-walled blood vessels without obvious necrosis and mitotic figures. Conclusion Pancreatic PEComas is a kind of undetermined biological behavior of mesenchymal tumors, more common in women, has its unique morphology and immunophenotype. The current complete surgical resection as the main treatment, should be followed up after surgery.