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髓系肉瘤(myeloid sarcoma,MS)又称粒细胞肉瘤(granulocytic sarcoma,GS),是原始或幼稚细胞的髓系细胞在髓外形成的实体肿瘤,可与急性髓系白血病(acute myeloid leukemia,AML)或骨髓异常增生综合征/骨髓增殖性疾病(myelodyplastic syndrome,MDS / myelodyplastic syndrome,MPN)同时发生,MS在AML中占2.5%~9.1%^[1]。