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周期性动眼神经麻痹(oculomotor palsy with cyclic spasms)是一种罕见的发育异常导致的疾病,表现为受累眼动眼神经支配的肌肉发生周期性痉挛和麻痹。Rampholdi于1884年首先报道为动眼-眼睑异常,此后国外陆续有数十例报道,迄今国内报道不到10 例。现报道1例如下。1 资料患儿男,5岁,因右眼睑下垂4年余来诊。患者在8个月常规检查时发现右眼眼裂较左眼小,右侧瞳孔散大,且对光反射消失, 当时未系统检查。此后患者母亲发现患儿右眼睑下垂,有时可突然睁开,但患儿不能自由控制右眼运动,在睡眠时右眼亦有自发运动。到外院眼科检查发现患者右眼外斜视,伴有右眼弱视。未治
Oculomotor palsy with cyclic spasms is a rare disease caused by dysplasia that manifests as cyclical spasms and paralysis of the muscles that are subject to oculomotor innervation. Rampholdi first reported in 1884 as eye movement - eyelid abnormalities, followed by dozens of foreign reports, so far less than 10 cases reported in the country. 1 case is reported below. 1 data children male, 5 years old, due to the right eyelid ptosis more than 4 years to visit. At 8 months of routine examination, the patient found that his right eye was smaller than his left eye and that his right pupil was dilated. The light reflex disappeared and was not systematically examined. Since then, the patient’s mother found the child’s right eyelid drooping, and sometimes can suddenly open, but the child can not freely control the right eye movement, the right eye also has spontaneous movement during sleep. To the hospital ophthalmic examination found that patients with right eye exotropia, accompanied by right-amblyopia. Not rule