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本文报告一例4岁男孩,患有“吕佛硫氏综合症”,呈现呼吸困难和两肺有弥散的结节性浸润阴影,血中嗜伊红细胞增多。(白细胞总数35.000—28000/立方毫米、嗜伊红细胞占71—90%)。在住院期间进行了全面的检查包括骨髓活检,结果阴性。用Prednison 30毫克/日治疗20天后,逐渐减量4周后停用。嗜伊红细胞降至5%。但停药二月后(即发病4个月后),疾病进一步发展,出现全身淋巴结胀大,肝脾明显肿大达肋下7厘米,全身有出血点和结合膜下出血、贫血、血小板减少、嗜伊红细胞占18%。通过淋巴结和骨髓活检。确定了淋巴肉瘤的诊断。吕佛硫氏综合症具有嗜伊红细胞增多和肺部浸润,许多疾病都可有此表现,但由淋巴肉瘤引起者,却甚为少见。
This article reports a 4-year-old boy with Lv-sulan’s syndrome presenting with dyspnea and diffuse nodular infiltrates in both lungs with increased eosinophilia in the blood. (Total number of white blood cells 35.000-28000 / cubic mm, eosinophil 71-90%). A complete examination during the hospitalization included a bone marrow biopsy with negative results. After treatment with Prednison 30 mg / day for 20 days, it is withdrawn by tapering for 4 weeks. Eosinophils dropped to 5%. However, withdrawal in February (ie, after 4 months of onset), the disease further development of systemic lymphadenopathy, liver and spleen was significantly enlarged up to 7 cm ribs, the body with bleeding and sub-membrane hemorrhage, anemia, thrombocytopenia , Eosinophilia accounted for 18%. Through the lymph nodes and bone marrow biopsy. To determine the diagnosis of lymphosarcoma. Lvf Sulfur syndrome with eosinophilia and lung infiltration, many diseases can have this performance, but caused by lymphosarcoma, but very rare.