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浆液性周边脉络膜、睫状体脱离合并非裂孔源性视网膜脱离认为是葡萄膜渗漏综合征(简称UES)。最近Gass假设UES的原因是巩膜不正常,致涡静脉阻塞,血管外的蛋白质不能排于眼外,由于涡静脉阻塞增加了组织的渗透压,结果发生脉络膜及视网膜慢性渗出性脱离。Hunter综合征由于粘多糖类的沉着,其巩膜异常肥厚而发生UES。报告1例男性Hunter综合征病人,26岁,视力逐渐减退,右眼视力为20/30,左眼为20/300。眼底:右眼重度视乳头水肿,后极部有点状色素沉着。全周轻度脉络膜脱离,无视网膜脱离。左
Serous peripheral choroid, ciliary body detachment associated with non-splitaneous retinal detachment is considered to be uveal leak syndrome (UES). Recently, Gass hypothesized that the cause of UES is abnormal sclera, vortex vein occlusion, extravascular proteins can not be excluded from the eye, due to vortex vein occlusion increased tissue osmotic pressure, resulting in choroidal and retinal chronic exudative detachment. Hunter syndrome due to mucopolysaccharidosis, the sclera abnormal hypertrophy and UES occurred. Reported a case of male Hunter syndrome patients, 26 years of age, visual acuity gradually decreased visual acuity of 20/30 for the left eye and 20/300 for the left eye. Fundus: Right eye severe papilledema, posterior pole a little pigmentation. Weekly mild choroidal detachment without retinal detachment. left