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马凡氏综合征是一种常染色体显性遗传的结缔组织疾病,在临床上较少见,但致残率极大,成人多死于心血管病变。本文通过对30例马凡氏综合征的心血管表现进行临床总结,探讨本病在心血管系统的临床表现,提高临床医师对本病在心血管异常方面的认识,并寻找本病的最佳诊断和治疗方法。1 资料和方法本组共30例患者,为我院1985年1月至2003
Marfan syndrome is an autosomal dominant genetic connective tissue disease, clinically rare, but the great disability, adult deaths from cardiovascular disease. In this paper, 30 cases of Marfan syndrome, cardiovascular manifestations of clinical summary to explore the clinical manifestations of the disease in the cardiovascular system to improve clinicians on the disease in cardiovascular awareness and to find the best diagnosis of the disease and treatment method. 1 Materials and Methods A total of 30 patients in this group, our hospital from January 1985 to 2003