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moyamoya病是一种比较少见的脑动脉纤维肌肉发育不良的一组疾病。其发病机理不明。特点是:颈内动脉最常在虹吸部和颈部发育不全,甚至于管腔完全闭塞和形成颈外颈内动脉的分枝相吻合的非典型的动脉网。同时由于血管壁无力而发生缺血性脑循环障碍或蛛网膜下腔出血。较少出现癫痫发作。如果考虑到此病在青年时即已出现,则采取预防和治疗措施以防止病情发展是必要的。由于脑缺乏充分需要的血流,使许多神经外科医生想到对moyamoya病可以将颅内颅外动脉显微吻合建立短路。Bodosi等认为,手术应在年青时进行,尽可能在出现稳定的神经症状以前进行为好。病例介绍如下:
Moyamoya disease is a relatively rare group of diseases of cerebral arterial fibromuscular dysplasia. Its pathogenesis is unknown. Characteristics are: most common in the sphincter sphincter and neck hypoplasia, and even complete lumen occlusion and the formation of external carotid artery branches atypical arterial network consistent. At the same time as a result of weakness of the vascular wall ischemic cerebral circulation disorder or subarachnoid hemorrhage. Fewer seizures. Taking into account that the disease has occurred in adolescence, it is necessary to take preventive and curative measures to prevent the progression of the disease. Due to the brain’s lack of adequately required blood flow, many neurosurgeons have come to think of a short circuit in micrometastasis of extracranial extracranial arteries for moyamoya disease. Bodosi et al. Concluded that surgery should be performed in young adults and as much as possible before stable neurological symptoms develop. Case description is as follows: