论文部分内容阅读
通过两例典型迟发性皮肤卟啉病。对卟啉病的定义、分类、迟发性皮肤卟啉病的诊断特点、治疗原则进行了介绍。讨论中着重提及某些迟发性皮肤卟啉病患者有明显家族倾向和青海隐性卟啉病并非罕见。鉴于高原地区紫外线幅射量大;红细胞增多症常见;溶血是否可使卟啉增多?!当地居民有大量饮酒习惯,有可能增加卟啉病的发病率。卟啉增多可增加对紫外线的敏感性,但高原人群皮肤色泽黑抵消了一部分紫外线作用,推测无症状(隐性)卟啉病患者并不少见。患者免疫学方面改变值得进一步探讨。
Passed two cases of typical delayed-onset skin porphyria. The definition and classification of porphyria, the diagnostic characteristics of delayed skin porphyria and the principle of treatment were introduced. In the discussion, it is not uncommon to mention that there are obvious familial tendencies in some patients with delayed skin porphyria and latent porphyria in Qinghai. In view of the high altitude ultraviolet radiation in the plateau; polycythemia common; hemolysis can make porphyrin increased? Local residents have a lot of drinking habits, may increase the incidence of porphyria. Increased porphyrins can increase the sensitivity of UV, but the skin of black people in high altitude to offset part of the UV effect, suggesting that asymptomatic (recessive) porphyria is not uncommon. Changes in patient immunology deserve further exploration.