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特发性肺含铁血黄素沉着症(以下简称IPH)系一少见病。其特征为肺内有含铁血黄素沉着而呈弥漫性阴影,且反复发作的呼吸道症状,咯血和低色素小细胞性贫血,痰中或胃液内可见含铁血黄素巨核细胞,棕色肺。病因与下列因素有关: 1、抗原抗体选择性地作用于肺泡引起出血。 2、肺循环压力周期性地增高。 3、遗传因素:肺组织先天性结构异常如弹力纤维减少及断裂。 4、肺泡有异常上皮细胞。 5、对牛奶蛋白过敏。笔者曾收治两名IPH患儿,病情介绍如下: 例一,女,10岁,因反复发热、咳嗽、痰
Idiopathic pulmonary hemosiderosis (hereinafter referred to as IPH) is a rare disease. It is characterized by the presence of hemosiderin in the lungs with diffuse shadow and repeated episodes of respiratory symptoms, hemoptysis and hypochromic small cell anemia, sputum or gastric juice visible hemosiderin megakaryocytes, brown lung. Etiology and the following factors: 1, antigen and antibody selectively act on alveolar hemorrhage. 2, pulmonary pressure increased periodically. 3, genetic factors: congenital lung tissue abnormalities such as elastic fibers to reduce and break. 4, alveolar abnormal epithelial cells. 5, allergic to milk protein. I had admitted two children with IPH, the condition is as follows: Example 1, female, 10 years old, due to repeated fever, cough, phlegm