First case report of Stevens-Johnson syndrome complicated with macrophage activation syndrome

• 作 者: 陈香元;曾华松;
• 机 构: 广州市妇女儿童医疗中心过敏免疫风湿病科
• 出 处: 中华医学生物免疫学会第二届学术年会
• 发表日期: 2014年期

　　Stevens-Johnson syndrome (SJS) is a complex immunological syndrome with high morbidityand mortality and characterized by acute blistering affecting the skin and at least twomucous membranes.Macrophage activation syndrome (MAS) is a severe,potentially life-threatening syndrome that often occurs in children and adults with autoimmune disease,especially systemic-onset juvenile idiopathic arthritis or adult-onset Still s disease.This case report highlights the potential risks of SJS developing into MAS,and suggests that rapid diagnosis and treatment are essential to achieving favorable outcomes.