Genetic analysis of inherited fibrinogen disorders in 43 patients and application of thrombelastogra

来源 :The 35th World Congress of the International Society of Hema | 被引量 : 0次 | 上传用户：jxczl900424

【摘要】

：

【作者】

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Jingyi Zhou Qiulan Ding Linlin Jiang Qi Ouyang Xuefeng Wang Xiaodong Xi Hongli Wang

【机构】

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State Key Laboratory of Medical Genomics,Shanghai Institute of Hematology,Ruijin Hospital,Shanghai J

【出处】

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The 35th World Congress of the International Society of Hema

【发表日期】

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2014年5期

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Background Hereditary fibrinogen disorders include quantitative abnormality (afibrinogenemia and hypofibrinogenemia),qualitative abnormality (dysfibrinogenemia) or both (hypo-dysfibrinogenemia).Inherited dysfibrinogenemia is characterized by reduced level of functional fibrinogen (Fg) but normal antigen level.

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Genetic analysis of inherited fibrinogen disorders in 43 patients and application of thrombelastogra

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